Abstract

Endometriosis affects 5%-10% of women in reproductive age and is usually localized in the pelvic and abdominal organs resulting in chronic pain, deep dyspareunia and infertility. Exceptionally, superficial endometriosis can lead to hemorrhagic abdominal effusion. Umbilical localization is considered a rare presentation, especially in its primary form. As there are many atypical cases, the differential diagnosis between endometriosis and other soft tissue tumors can be quite difficult. We report a historical case associating primary umbilical endometriosis and hemorrhagic ascites and discuss the probable pathogenic hypotheses and difficulties related to the diagnosis.