Primary breast lymphoma (PBL) is an uncommon and curable disease. It usually presents as a clinically palpable mass and is rarely detected in screening. Although the imaging characteristics are not specific, they may sometimes mimic benign masses. However, the clinical and imaging findings in PBL can mimic those of breast carcinoma, and sometimes, its presentation is suggestive of inflammatory breast cancer. Diagnosis depends on adequate tissue sampling for histology examination and immunophenotyping. Unlike primary breast carcinoma, surgery is not the key treatment for PBL. Treatment is mainly confined to combination of chemotherapy and radiation therapy.