Abstract

Background: Sex cord tumor with annular tubules (SCTAT) is an uncommon ovarian tumor. One third of the cases are related with hyperestrogenism and Peutz-Jeghers syndrome (PJS). They are mostly seen in reproductive period and only rarely in pediatric patient group. Here, we present a 12 years old patient with SCTAT with a review of related literature.

Case Report: In a patient operated with a pre-diagnosis of acute appendicitis, a mass was found out in the right ovary. An appendectomy and right salpingooophorectomy were performed. In cross section of ovary, regular-bordered tumoral mass of nearly 6x5 cm with white-colored millimetric nodular foci and rare hemorrhagic areas were observed. Depending on histopathological and immunohistochemical findings, the diagnosis was SCTAT.

Conclusion: This case is worth discussing since besides being an infrequent entity, SCTAT is also very rare in pediatric age.